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Case Report Special Issue Lymphology & Phlebology
Primary sjogren‘s syndrome in a child
Gabriela Ivankovich Escoto
Received: January 01, 1971 | Published: November 26, 2018
Citation: Escoto GI. Primary sjogren‘s syndrome in a child. MOJ Immunol. 2018;6(6):223-22 4. DOI: 10.15406/moji.2018.06.00232
Abstract
Sjogren´s syndrome is an autoimmune exocrinopathy of unknown aetiology characterized by xerostomy and y xerophtalmia or keratoconjunctivitis sicca. It might be a primary condition, which is rare during infancy. It is usually secondary, in most cases due to autoimmunity (systemic lupuserythematous, rheumatoid arthritis and others). There is a polyclonal reaction with positive antinuclear antibodies, anti-Ro/SS-A and anti-La/SS-B due to B cell hyperstimulation. This case is of a 16-year-old female with autoimmune thrombocytopenia as initial manifestation, and a serology that suggests recent Epstein-Barr virus infection as a possible trigger. She has had recurrent parotiditis, multiple dental cavities and keratoconjuntivitis with positive antinuclear antibody, positive anti-Ro/SS-A and hypocomplementemia. She was diagnosed as a primary Sjogren´s syndrome and received a short course of steroids and hydroxychloroquine with a good clinical response.
Keywords: Sjogren syndrome, Autoimmunity, Exocrinopathy, Immunoglobulin, Auto antibodies, Errythro sedimentation rate, Haematology, Hydroxychloroquine, Immunodeficiency, Lymphadenopathy, Leucopoenia, Lymphopenia, Cryoglobulinaemia, Vasculitis
©2018 Escoto. This is an open access article distributed under the terms of the, which permits unrestricted use, distribution, and build upon your work non-commercially.
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